Dandy-Walker Malformation in an Asymptomatic 27-Year-Old Woman. A Case Report

  • Joyce Antonella Jiménez Universidad Católica de Santiago de Guayaquil, Guayaquil, Ecuador.
  • Daniel Francisco Landívar Universidad Católica de Santiago de Guayaquil, Guayaquil, Ecuador.
  • Fernando Xavier Posligua Universidad Católica de Santiago de Guayaquil, Guayaquil, Ecuador.
  • Jorge Rigoberto González Universidad Católica de Santiago de Guayaquil, Guayaquil, Ecuador.
Keywords: Dandy-Walker Syndrome, Dandy-Walker Variant, Hydrocephalus, Cerebellar Vermis Hypoplasia

Abstract

Introduction: Dandy-Walker malformation (DWM) is a rare congenital disorder that involves the cerebellum and fourth ventricle. Incidentally detected asymptomatic DWM is sparsely reported in literature at extremes of age (from 1 to 75 years) in association with different diseases. We aim to report the case of a patient with an incidental finding of a DWM after a road traffic accident, reinforcing the importance of suspicion, investigation, diagnosis of clinical presentations. The Case: This case report describes a 27-year-old female patient who presented to the emergency room after a motor vehicle collision. She suffered a left kidney and spleen injury. The patient’s brain CT scan revealed an enlarged cisterna magna with normal cerebellum, partial hypoplasia of the cerebellar vermis and enlargement of the fourth ventricle compatible with DWM. Neurological examination was unremarkable. An exploratory laparotomy was performed, and the left kidney and spleen showed hemorrhage, so a left nephrectomy and splenectomy was done. Conclusions: This case report aimed to characterize the DWM, which is a congenital malformation of the central nervous system. Asymptomatic patients do not require surgical treatment; however, these patients should be followed up once a year.

Author Biography

Joyce Antonella Jiménez, Universidad Católica de Santiago de Guayaquil, Guayaquil, Ecuador.

Joyce Antonella Jiménez is a recently graduated MD at Universidad Católica de Santiago de Guayaquil. She is currently studying for the United States Medical Licensing Examination to pursue her career in the neurology field.

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Published
2018-11-07
How to Cite
Jiménez, J., Landívar, D., Posligua, F., & González, J. (2018). Dandy-Walker Malformation in an Asymptomatic 27-Year-Old Woman. A Case Report. International Journal of Medical Students, 6(3), 110-113. Retrieved from http://www.ijms.info/index.php/IJMS/article/view/267
Section
Case Report